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Authors: Avramenko I.

Pages: 63-69


Congenital development defects (CDD) are a difficult medical and much more social problem. They are observed in 3-5% of newborns and are a cause of 20% infant deaths. The opportunity of modern ex-amination methods as well as improvement in operative technique and perioperative care and rehabilitation gave a chance to improve considerably the results of CDD patient treatment. However, CDD is further one of main lethality causes of newborns, infants and children of early years as well as one of key causes of children’s disability. It is not always able to make a full correction of congenital multiple development defects. Alternate surgical treatment depends mainly on defect constituents and hospital potentials. Therefore, treatment algorithm of different combined development defects is not finally developed and under discussion.

The aim of our research is to analyse the results of treatment and priority of helping children with congenital multiple development defects, among of which there is a heart defect.

It is done a retrospective analysis of medical documents on children with congenital multiple development defects and congenital heart defects at the age of less than one year. All results were statistically worked out by means of an original computer program Microsoft Ex-cel.

Most of all congenital heart defects are combined with anomalies of the urinary system and the gastrointestinal tract, rarely they are combined with development defects of the nervous system, a skeleton and respiratory organs. The anomaly of a skeleton and the urinary sys-tem influences rarely on a patient status, but does not need emergency surgical treatment. Critical congenital heart defects at CDD require surgical treatment first of all. Noncritical congenital heart defects influence on the course of postsurgical period and are to be taken into consideration while children with CCD undergo the treatment. The anomaly of the gastrointestinal tract is crucial in the destabilization of a patient clinical state and needs surgical treatment in the very period of newbornness. Considerably higher mortality after surgical treatment is connected with doing palliative operations, but not with completed correction of development defects.

Carrying out a research of multiple organ congenital anomalies makes it able to understand better aetiology and pathogenesis of their occurrence; moreover the profound analysis of the treatment provided makes it able to set priorities of helping such patients.

Key words: congenital multiple development defects, congenital heart defects, children.

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